Double Outlet Right Ventricle
DORV; Dextroposed aorta; Overriding aorta; Taussig-Bing anomaly; Tetralogy of Fallot
Definition and Characteristics
DORV encompasses a range of heart defects, in which the great vessels are misaligned with respect to the ventricles. Normally the pulmonary trunk arises from the right ventricle (RV) and aorta from the left ventricle (LV). In DORV, both the pulmonary artery and the aorta arise completely or mostly from the RV. If the aorta obtains 50% of its blood from the RV, the defect is classified as DORV . Because both outflow vessels originate predominately from the RV, there is a concomitant ventricular septal defect (VSD).